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教育部委託研究計畫      計畫執行:國立臺灣大學圖書館
 
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機構 日期 題名 作者
臺大學術典藏 2018-09-10T14:50:14Z Efficacy and safety of intermittent hemodialysis in infants and young children with inborn errors of metabolism 胡務亮;吳恩婷;蔡宜蓉;黃書健;李妮鍾;簡穎秀;曹永魁; Tsai, I.-J. and Hwu, W.-L. and Huang, S.-C. and Lee, N.-C. and Wu, E.-T. and Chien, Y.-H. and Tsau, Y.-K.; Tsai, I-Jung;Hwu, Wuh-Liang;Huang, Shu-Chien;Lee, Ni-Chung;Wu, En-Ting;Chien, Yin-Hsiu;Tsau, Yong-Kwei; Tsai, I-Jung; NI-CHUNG LEE; Hwu, Wuh-Liang; YONG-KWEI TSAU; Huang, Shu-Chien; I-JUNG TSAI; YIN-HSIU CHIEN; Lee, Ni-Chung; SHU-CHIEN HUANG; Wu, En-Ting; Chien, Yin-Hsiu; WUH-LIANG HWU; Tsau, Yong-Kwei; EN-TING WU
臺大學術典藏 2018-09-10T09:51:20Z Long-term follow-up results in patients with classic infantile Pompe disease receiving enzyme therapy since newborn Yin-Hsiu Chien and Wuh-Liang Hwu and Ni-Chung Lee and Chun-An Chen and Fuu-Jen Tsai and Wen-Hui Tsai and Hsiang-Ju Huang and Wei-Chung Hsu and Tzu-Hsun Tsai and Jeng-Yi Shieh; Chien, Yin-Hsiu;Hwu, Wuh-Liang;Lee, Ni-Chung;Chen, Chun-An;Tsai, Fuu-Jen;Tsai, Wen-Hui;Huang, Hsiang-Ju;Hsu, Wei-Chung;Tsai, Tzu-Hsun;Shieh, Jeng-Yi; 胡務亮 ;蔡紫薰 ;許巍鐘 ;陳俊安 ;李妮鍾 ;簡穎秀 ;謝正宜; Chien, Yin-Hsiu; YIN-HSIU CHIEN; Hwu, Wuh-Liang; Lee, Ni-Chung; Chen, Chun-An; Tsai, Fuu-Jen; Tsai, Wen-Hui; Huang, Hsiang-Ju; Hsu, Wei-Chung; Tsai, Tzu-Hsun; Shieh, Jeng-Yi
臺大學術典藏 2018-09-10T09:40:31Z Myostatin and Insulin-Like Growth Factor I: Potential Therapeutic Biomarkers for Pompe Disease Chien, Yin-Hsiu;Han, Der-Sheng;Hwu, Wuh-Liang;Thurberg, Beth L.;Yang, Wei-Shiung; Chien, Yin-Hsiu;Han, Der-Sheng;Hwu, Wuh-Liang;Thurberg, Beth L.;Yang, Wei-Shiung; Chien, Y.-H. and Han, D.-S. and Hwu, W.-L. and Thurberg, B.L. and Yang, W.-S.; 胡務亮 ;簡穎秀 ;楊偉勛; 胡務亮 ;簡穎秀 ;楊偉勛; Chien, Yin-Hsiu; WEI-SHIUNG YANG; YIN-HSIU CHIEN; Han, Der-Sheng; Han, Der-Sheng; Hwu, Wuh-Liang; Hwu, Wuh-Liang; DER-SHENG HAN; WUH-LIANG HWU; Thurberg, Beth L.; Yang, Wei-Shiung; Yang, Wei-Shiung
臺大學術典藏 2018-09-10T09:40:30Z Promising outcomes in glutaric aciduria type i patients detected by newborn screening Lee, Chee-Seng;Chien, Yin-Hsiu;Peng, Shinn-Forng;Cheng, Pin-Wen;Chang, Lih-Maan;Huang, Ai-Chu;Hwu, Wuh-Liang;Lee, Ni-Chung; Lee, C.-S. and Chien, Y.-H. and Peng, S.-F. and Cheng, P.-W. and Chang, L.-M. and Huang, A.-C. and Hwu, W.-L. and Lee, N.-C.; 胡務亮 ;彭信逢 ;李妮鍾 ;黃愛珠 ;簡穎秀; NI-CHUNG LEE; Lee, Chee-Seng; YIN-HSIU CHIEN; Chien, Yin-Hsiu; WUH-LIANG HWU; Peng, Shinn-Forng; Cheng, Pin-Wen; Chang, Lih-Maan; Huang, Ai-Chu; Hwu, Wuh-Liang; Lee, Ni-Chung; �^�H�{
臺大學術典藏 2018-09-10T09:16:21Z A novel 3670-base pair mitochondrial DNA deletion resulting in multi-systemic manifestations in a child Liu, Hsin-Ming;Tsai, Li-Ping;Chien, Yin-Hsiu;Wu, Jia-Feng;Weng, Wen-Chin;Peng, Shinn-Forng;Wu, En-Ting;Huang, Pei-Hsin;Lee, Wang-Tso;Tsai, I-Jun;Hwu, Wuh-Liang;Lee, Ni-Chung; Liu, H.-M. and Tsai, L.-P. and Chien, Y.-H. and Wu, J.-F. and Weng, W.-C. and Peng, S.-F. and Wu, E.-T. and Huang, P.-H. and Lee, W.-T. and Tsai, I.-J. and Hwu, W.-L. and Lee, N.-C.; 胡務亮 ;彭信逢 ;吳恩婷 ;吳嘉峰 ;蔡宜蓉 ;李旺祚 ;李妮鍾 ;簡穎秀 ;黃佩欣 ;翁妏謹; NI-CHUNG LEE; Liu, Hsin-Ming; WANG-TSO LEE; Tsai, Li-Ping; WEN-CHIN WENG; Chien, Yin-Hsiu; JIA-FENG WU; Wu, Jia-Feng; YIN-HSIU CHIEN; Weng, Wen-Chin; Peng, Shinn-Forng; I-JUNG TSAI; Wu, En-Ting; WUH-LIANG HWU; Huang, Pei-Hsin; PEI-HSIN HUANG; EN-TING WU; Lee, Wang-Tso; Tsai, I-Jun; Hwu, Wuh-Liang; Lee, Ni-Chung; �^�H�{
臺大學術典藏 2018-09-10T09:14:34Z Early pathologic changes and responses to treatment in patients with later-onset Pompe disease Chien, Yin-Hsiu;Lee, Ni-Chung;Huang, Pei-Hsin;Lee, Wang-Tso;Thurberg, Beth L.;Hwu, Wuh-Liang; Chien, Y.-H. and Lee, N.-C. and Huang, P.-H. and Lee, W.-T. and Thurberg, B.L. and Hwu, W.-L.; 胡務亮 ;李妮鍾 ;簡穎秀 ;黃佩欣; NI-CHUNG LEE; Chien, Yin-Hsiu; WANG-TSO LEE; Lee, Ni-Chung; YIN-HSIU CHIEN; Huang, Pei-Hsin; WUH-LIANG HWU; Lee, Wang-Tso; Thurberg, Beth L.; PEI-HSIN HUANG; Hwu, Wuh-Liang
臺大學術典藏 2018-09-10T09:14:30Z Genome-wide gene expression analysis implicates the immune response and lymphangiogenesis in the pathogenesis of fetal chylothorax Yeang, C.-H. and Ma, G.-C. and Shih, J.-C. and Yang, Y.-S. and Chen, C.-P. and Chang, S.-P. and Wu, S.-H. and Liu, C.-S. and Kuo, S.-J. and Chou, H.-C. and Hwu, W.-L. and Cameron, A.D. and Ginsberg, N.A. and Lin, Y.-S. and Chen, M.; Yeang, Chen-Hsiang;Ma, Gwo-Chin;Shih, Jin-Chung;Yang, Yu-Shih;Chen, Chih-Ping;Chang, Shun-Ping;Wu, Sheng-Hai;Liu, Chin-San;Kuo, Shou-Jen;Chou, Hung-Chieh;Hwu, Wuh-Liang;Cameron, Alan D.;Ginsberg, Norman A.;Lin, Yi-Shing;Chen, Ming; 楊友仕 ;施景中 ;胡務亮 ;周弘傑 ;陳明; HUNG-CHIEH CHOU; Yeang, Chen-Hsiang; Ma, Gwo-Chin; MING CHEN; YU-SHIH YANG; Shih, Jin-Chung; JIN-CHUNG SHIH; Yang, Yu-Shih; WUH-LIANG HWU; Chen, Chih-Ping; Chang, Shun-Ping; Wu, Sheng-Hai; Liu, Chin-San; Kuo, Shou-Jen; Chou, Hung-Chieh; Hwu, Wuh-Liang; Cameron, Alan D.; Ginsberg, Norman A.; Lin, Yi-Shing; Chen, Ming
臺大學術典藏 2018-09-10T08:22:12Z 遺傳檢測倫理議題及遺傳諮詢倫理準則 蔡甫昌(Daniel Fu-Chang Tsai);楊尚儒(Shang-Ju Yang);張至寧Chih-Ning Chang);胡務亮(Wuh-Liang Hwu);楊智超(Chih-Chao Yang); 蔡甫昌;楊尚儒;張至寧;胡務亮;楊智超; TSAI, FU-CHANG;YANG, SHANG-JU;CHANG, CHIH-NING;HWU, WUH-LIANG;YANG, CHIH-CHAO; 蔡甫昌; WUH-LIANG HWU; 楊尚儒; 張至寧; 胡務亮; 楊智超
臺大學術典藏 2018-09-10T07:43:55Z Clinical features of AADC-deficient children and therapeutic prospects Wuh-Liang Hwu and Yin-Hsiu Chien and Ni-Chung Lee and Wang-Tso Lee and Ruey-Meei Wu; 胡務亮;簡穎秀;李妮鍾;李旺祚;吳瑞美; HWU, WUH-LIANG;CHIEN, YIN-HSIU;LEE, NI-CHUNG;LEE, WANG-TSO;WU, RUEY-MEEI; YIN-HSIU CHIEN; HWU, WUH-LIANG; CHIEN, YIN-HSIU; LEE, NI-CHUNG; LEE, WANG-TSO; WU, RUEY-MEEI
臺大學術典藏 2018-09-10T07:04:16Z Bone marrow transplantation results in donor-derived hepatocytes in an animal model of inherited cholestatic liver disease YUNG-MING JENG; Hui-Ling Chen; HUEY-LING CHEN; WUH-LIANG HWU; CHEN, HUEY-LING; CHEN, HUI-LING; HWU, WUH-LIANG; JENG, YUNG-MING; CHANG, MEI-HWEI; Chen, H.-L. and Wang, R. and Chen, H.-L. and Hwu, W.-L. and Jeng, Y.-M. and Chang, M.-H. and Ling, V.; 陳慧玲;陳惠玲;胡務亮;鄭永銘;張美惠; CHEN, HUEY-LING;CHEN, HUI-LING;HWU, WUH-LIANG;JENG, YUNG-MING;CHANG, MEI-HWEI; MEI-HWEI CHANG

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