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臺灣學術機構典藏系統 (Taiwan Academic Institutional Repository, TAIR)
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Institution Date Title Author
國立成功大學 2025-04-19 應用層級分析法探討光電產業中SMT(Surface-mount technology)製程導入AMHS自動化發料系統關鍵成功因素之研究 林相羽; Lin, Hsiang-Yu
臺大學術典藏 2021-09-14T23:19:08Z Molecular basis of mucopolysaccharidosis IVA (Morquio A syndrome): A review and classification of GALNS gene variants and reporting of 68 novel variants Zanetti, Alessandra; D'Avanzo, Francesca; AlSayed, Moeenaldeen; Brusius-Facchin, Ana Carolina; YIN-HSIU CHIEN; Giugliani, Roberto; Izzo, Emanuela; Kasper, David C.; Lin, Hsiang Yu; Lin, Shuan Pei; Pollard, Laura; Singh, Akashdeep; Tonin, Rodolfo; Wood, Tim; Morrone, Amelia; Tomanin, Rosella
臺大學術典藏 2020-02-10T09:00:35Z Causes of death and clinical characteristics of 34 patients with Mucopolysaccharidosis II in Taiwan from 1995-2012 Lin, Hsiang-Yu; Chuang, Chih-Kuang; Huang, Yu-Hsiu; Tu, Ru-Yi; Lin, Fang-Ju; Lin, Shio Jean; Chiu, Pao Chin; Niu, Dau-Ming; Tsai, Fuu-Jen; Hwu, Wuh-Liang; Chien, Yin-Hsiu; Lin, Ju-Li; Chou, Yen-Yin; Tsai, Wen-Hui; Chang, Tung-Ming; Lin, Shuan-Pei; SHAU-PING LIN
臺大學術典藏 2020-02-10T09:00:35Z Long-term galsulfase enzyme replacement therapy in Taiwanese mucopolysaccharidosis VI patients: A case series Lin, Hsiang-Yu; Chuang, Chih-Kuang; Wang, Chung-Hsing; Chien, Yin-Hsiu; Wang, Yu-Mei; Tsai, Fuu-Jen; Chou, Yen-Yin; Lin, Shio Jean; Pan, Hui-Ping; Niu, Dau-Ming; Hwu, Wuh-Liang; Ke, Yu-Yuan; Lin, Shuan-Pei; SHAU-PING LIN
臺大學術典藏 2020-02-10T09:00:35Z Cardiac structure and function and effects of enzyme replacement therapy in patients with mucopolysaccharidoses I, II, IVA and VI Lin, Hsiang-Yu; Chuang, Chih-Kuang; Chen, Ming-Ren; Lin, Shan-Miao; Hung, Chung-Lieh; Chang, Chia-Ying; Chiu, Pao Chin; Tsai, Wen-Hui; Niu, Dau-Ming; Tsai, Fuu-Jen; Lin, Shio Jean; Hwu, Wuh-Liang; Lin, Ju-Li; Lin, Shuan-Pei; SHAU-PING LIN
臺大學術典藏 2020-02-10T09:00:34Z Clinical characteristics and surgical history of Taiwanese patients with mucopolysaccharidosis type II: data from the hunter outcome survey (HOS) Lin, Hsiang-Yu; Chuang, Chih-Kuang; Chen, Ming-Ren; Lin, Shio Jean; Chiu, Pao Chin; Niu, Dau-Ming; Tsai, Fuu-Jen; Hwu, Wuh-Liang; Chien, Yin-Hsiu; Lin, Ju-Li; Lin, Shuan-Pei; SHAU-PING LIN
國立交通大學 2020-02-02T23:54:29Z Relationships among Height, Weight, Body Mass Index, and Age in Taiwanese Children with Different Types of Mucopolysaccharidoses Lin, Hsiang-Yu; Lee, Chung-Lin; Chiu, Pao Chin; Niu, Dau-Ming; Tsai, Fuu-Jen; Hwu, Wuh-Liang; Lin, Shio Jean; Lin, Ju-Li; Chang, Tung-Ming; Chuang, Chih-Kuang; Lin, Shuan-Pei
國立交通大學 2020-02-02T23:54:29Z An At-Risk Population Screening Program for Mucopolysaccharidoses by Measuring Urinary Glycosaminoglycans in Taiwan Lin, Hsiang-Yu; Lee, Chung-Lin; Lo, Yun-Ting; Tu, Ru-Yi; Chang, Ya-Hui; Chang, Chia-Ying; Chiu, Pao Chin; Chang, Tung-Ming; Tsai, Wen-Hui; Niu, Dau-Ming; Chuang, Chih-Kuang; Lin, Shuan-Pei
臺大學術典藏 2019-10-14T05:56:44Z Methylmalonic acidemia/propionic acidemia - the biochemical presentation and comparing the outcome between liver transplantation versus non-liver transplantation groups Niu, Dau-Ming;MING-CHIH HO;REY-HENG HU;Liu, Chin-Su;Lin, Shuan-Pei;NI-CHUNG LEE;WUH-LIANG ​​HWU;Yang, Chia-Feng;Lin, Niang-Cheng;Chiang, Chuan-Chi;Lai, Chih-Jou;Ho, Huey-Jane;Liao, Hsuan-Chieh;Lin, Hsiang-Yu;YIN-HSIU CHIEN;Chu, Tzu-Hung; Chu, Tzu-Hung; YIN-HSIU CHIEN; Lin, Hsiang-Yu; Liao, Hsuan-Chieh; Ho, Huey-Jane; Lai, Chih-Jou; Chiang, Chuan-Chi; Lin, Niang-Cheng; Yang, Chia-Feng; WUH-LIANG ??HWU; NI-CHUNG LEE; Lin, Shuan-Pei; Liu, Chin-Su; REY-HENG HU; MING-CHIH HO; Niu, Dau-Ming
國立交通大學 2019-09-02T07:46:11Z Functional independence of Taiwanese patients with mucopolysaccharidoses Lee, Chung-Lin; Lin, Hsiang-Yu; Chuang, Chih-Kuang; Chiu, Huei-Ching; Tu, Ru-Yi; Huang, You-Hsin; Hwu, Wuh-Liang; Tsai, Fuu-Jen; Chiu, Pao-Chin; Niu, Dau-Ming; Chen, Yann-Jang; Chao, Mei-Chyn; Chang, Tung-Ming; Lin, Ju-Li; Chang, Chia-Ying; Kao, Yu-Chia; Lin, Shuan-Pei
國立交通大學 2019-08-02T02:18:30Z Cardiac characteristics and natural progression in Taiwanese patients with mucopolysaccharidosis III Lin, Hsiang-Yu; Chen, Ming-Ren; Lin, Shan-Miao; Hung, Chung-Lieh; Niu, Dau-Ming; Chang, Tung-Ming; Chuang, Chih-Kuang; Lin, Shuan-Pei
國立交通大學 2019-04-03T06:36:12Z Plasmonic Gold Nanorods Coverage Influence on Enhancement of the Photoluminescence of Two-Dimensional MoS2 Monolayer Lee, Kevin C. J.; Chen, Yi-Huan; Lin, Hsiang-Yu; Cheng, Chia-Chin; Chen, Pei-Ying; Wu, Ting-Yi; Shih, Min-Hsiung; Wei, Kung-Hwa; Li, Lain-Jong; Chang, Chien-Wen
國立交通大學 2019-04-02T06:00:47Z Mucopolysaccharidosis III in Taiwan: Natural history, clinical and molecular characteristics of 28 patients diagnosed during a 21-year period Lin, Hsiang-Yu; Chuang, Chih-Kuang; Lee, Chung-Lin; Tu, Ru-Yi; Lo, Yun-Ting; Chiu, Pao Chin; Niu, Dau-Ming; Fang, Yi-Ya; Chen, Tzu-Lin; Tsai, Fuu-Jen; Hwu, Wuh-Liang; Lin, Shio Jean; Chang, Tung-Ming; Lin, Shuan-Pei
臺大學術典藏 2019 Long-term effects of enzyme replacement therapy for Taiwanese patients with mucopolysaccharidosis IVA Chuang, Chih-Kuang; Lin, Hsiang-Yu; Lin, Hsiang-Yu;Chuang, Chih-Kuang;Ke, Yu-Yuan;Hsu, Chia-Chi;Chiu, Pao Chin;Niu, Dau-Ming;Tsai, Fuu-Jen;Hwu, Wuh-Liang;Lin, Ju-Li;Lin, Shuan-Pei; Ke, Yu-Yuan; Hsu, Chia-Chi; Chiu, Pao Chin; Niu, Dau-Ming; Tsai, Fuu-Jen; Hwu, Wuh-Liang; Lin, Ju-Li; Lin, Shuan-Pei; SHAU-PING LIN
臺大學術典藏 2018-09-10T15:37:01Z Causes of death and clinical characteristics of 34 patients with Mucopolysaccharidosis II in Taiwan from 1995-2012 Dr. Segolene Ayme Lin, Hsiang-Yu;Chuang, Chih-Kuang;Huang, Yu-Hsiu;Tu, Ru-Yi;Lin, Fang-Ju;Lin, Shio Jean;Chiu, Pao Chin;Niu, Dau-Ming;Tsai, Fuu-Jen;Hwu, Wuh-Liang;Chien, Yin-Hsiu;Lin, Ju-Li;Chou, Yen-Yin;Tsai, Wen-Hui;Chang, Tung-Ming;Lin, Shuan-Pei; Lin, H.-Y. and Chuang, C.-K. and Huang, Y.-H. and Tu, R.-Y. and Lin, F.-J. and Lin, S.J. and Chiu, P.C. and Niu, D.-M. and Tsai, F.-J. and Hwu, W.-L. and Chien, Y.-H. and Lin, J.-L. and Chou, Y.-Y. and Tsai, W.-H. and Chang, T.-M. and Lin, S.-P.; 胡務亮;簡穎秀; YIN-HSIU CHIEN; Lin, Hsiang-Yu; Chuang, Chih-Kuang; WUH-LIANG HWU; Huang, Yu-Hsiu; Tu, Ru-Yi; Lin, Fang-Ju; Lin, Shio Jean; Chiu, Pao Chin; Niu, Dau-Ming; Tsai, Fuu-Jen; Hwu, Wuh-Liang; Chien, Yin-Hsiu; Lin, Ju-Li; Chou, Yen-Yin; Tsai, Wen-Hui; Chang, Tung-Ming; Lin, Shuan-Pei
亞洲大學 2017-01 Degradation of polylactic acid by irradiation 林湘瑜;Lin, Hsiang-Yu;林駿憑;LIN, CHUN-PING;*
國立成功大學 2016-06-27 Causes of death and clinical characteristics of 34 patients with Mucopolysaccharidosis II in Taiwan from 1995-2012 Lin, Hsiang-Yu;Chuang, Chih-Kuang;Huang, Yu-Hsiu;Tu, Ru-Yi;Lin, Fang-Ju;Lin, Shio Jean;Chiu, Pao Chin;Niu, Dau-Ming;Tsai, Fuu-Jen;Hwu, Wuh-Liang;Chien, Yin-Hsiu;Lin, Ju-Li;Chou, Yen-Yin;Tsai, Wen-Hui;Chang, Tung-Ming;Lin, Shuan-Pei
國立成功大學 2016-06 Long-term galsulfase enzyme replacement therapy in Taiwanese mucopolysaccharidosis VI patients: A case series Lin, Hsiang-Yu; Chuang, Chih-Kuang; Wang, Chung-Hsing; Chien, Yin-Hsiu; Wang, Yu-Mei; Tsai, Fuu-Jen; Chou, Yen-Yin; Lin, Shio Jean; Pan, Hui-Ping; Niu, Dau-Ming; Hwu, Wuh-Liang; Ke, Yu-Yuan; Lin, Shuan-Pei
國立臺灣大學 2016 Cardiac structure and function and effects of enzyme replacement therapy in patients with mucopolysaccharidoses I, II, IVA and VI Lin, Hsiang-Yu; Chuang, Chih-Kuang; Chen, Ming-Ren; Lin, Shan-Miao; Hung, Chung-Lieh; Chang, Chia-Ying; Chiu, Pao Chin; Tsai, Wen-Hui; Niu, Dau-Ming; Tsai, Fuu-Jen; Lin, Shio Jean; Hwu, Wuh-Liang; Lin, Ju-Li; Lin, Shuan-Pei; 胡務亮
國立臺灣大學 2016 Causes of death and clinical characteristics of 34 patients with Mucopolysaccharidosis II in Taiwan from 1995-2012 Lin, Hsiang-Yu; Chuang, Chih-Kuang; Huang, Yu-Hsiu; Tu, Ru-Yi; Lin, Fang-Ju; Lin, Shio Jean; Chiu, Pao Chin; Niu, Dau-Ming; Tsai, Fuu-Jen; Hwu, Wuh-Liang; Chien, Yin-Hsiu; Lin, Ju-Li; Chou, Yen-Yin; Tsai, Wen-Hui; Chang, Tung-Ming; Lin, Shuan-Pei; 胡務亮; 簡穎秀
國立交通大學 2014-12-12T02:44:07Z 利用金奈米柱提升單層與三層之二硫化鉬的電致發光與光致螢光 林祥宇; Lin, Hsiang-Yu; 施閔雄; Shih, Min-Hsiung
國立交通大學 2014-12-12T02:37:51Z 新穎垂直通道無接面薄膜電晶體之模擬研究 林香瑜; Lin,Hsiang-Yu; 趙天生; Chao,Tien-Sheng
國立交通大學 2014-12-12T01:59:53Z 容積陰影的時間適應性取樣演算法 林相宇; Lin, Hsiang-Yu; 施仁忠; Shih, Zen-Chung
國立交通大學 2014-12-08T15:34:15Z Adaptive sampling approach for volumetric shadows in dynamic scenes Lin, Hsiang-Yu; Chang, Chin-Chen; Tsai, Yu-Ting; Way, Der-Lor; Shih, Zen-Chung
國立臺灣大學 2014 Natural history and clinical assessment of Taiwanese patients with mucopolysaccharidosis IVA Lin, Hsiang-Yu; Chuang, Chih-Kuang; Chen, Ming-Ren; Chiu, Pao Chin; Ke, Yu-Yuan; Niu, Dau-Ming; Tsai, Fuu-Jen; Hwu, Wuh-Liang; Lin, Ju-Li; Lin, Shuan-Pei; 胡務亮
國立臺灣大學 2013 Enzyme replacement therapy for mucopolysaccharidosis VI-experience in Taiwan (vol 98, pg 72, 2009) Lin, Hsiang-Yu; Chen, Ming-Ren; Chuang, Chih-Kuang; Chen, Chih-Ping; Lin, Dar-Shong; Chien, Yin-Hsiu; Ke, Yu-Yuan; Tsai, Fuu-Jen; Pan, Hui-Ping; Lin, Shio-Jean; Hwu, Wuh-Liang; Niu, Dau-Ming; Lee, Ni-Chung; Lin, Shuan-Pei; 胡務亮; 李妮鍾; 簡穎秀
國立臺灣大學 2010 Newborn Screening for Methylmalonic Aciduria by Tandem Mass Spectrometry: 7 Years' Experience from Two Centers in Taiwan 鄭康祥; 劉美英; 高銓宏; 陳燕彰; 蕭廣仁; 劉孜孜; 林翔宇; 牛道明; 江傳箕; 林如立; 林炫沛; 李妮鍾; 胡務亮; CHENG, KANG-HSIANG; LIU, MEI-YING; KAO, CHUAN-HONG; CHEN, YANN-JANG; HSIAO, KWANG-JEN; LIU, TZE-TZE; LIN, HSIANG-YU; NIU, DAU-MING; CHIANG, CHUAN-CHI; LIN, JU-LI; LIN, SHUAN-PEI; LEE, NI-CHUNG; HWU, WUH-LIANG
國立成功大學 2009-05 Incidence of the Mucopolysaccharidoses in Taiwan, 1984-2004 Lin, Hsiang-Yu; Lin, Shuan-Pei; Chuang, Chih-Kuang; Niu, Dau-Ming; Chen, Ming-Ren; Tsai, Fuu-Jen; Chao, Mei-Chyn; Chiu, Pao-Ching; Lin, Shio-Jean; Tsai, Li-Ping; Hwu, Wuh-Liang; Lin, Ju-Li
國立成功大學 2008-06 Effects of growth hormone treatment on height, weight, and obesity in Taiwanese patients with Prader-Willi syndrome Lin, Hsiang-Yu; Lin, Shuan-Pei; Tsai, Li-Ping; Chao, Mei-Chyn; Chen, Ming-Ren; Chuang, Chih-Kuang; Huang, Chi-Yu; Tsai, Fuu-Jen; Chou, I-Ching; Chiu, Pao-Ching; Huang, Cheng-Hung; Yen, Jui-Lung; Lin, Ju-Li; Kuo, Pao-Lin
國立臺灣大學 2008 X-Linked Myotubular Myopathy with a Novel Mtm1 Mutation in a Taiwanese Child 張家穎; 林炫沛; 林翔宇; 莊志光; 何啟生; 蘇怡寧; CHANG, CHIA-YING; LIN, SHUAN-PEI; LIN, HSIANG-YU; CHUANG, CHIH-KUANG; HO, CHE-SHENG; SU, YI-NING
國立成功大學 2007-06 Prader-Willi syndrome in Taiwan Lin, Hsiang-Yu; Lin, Shuan-Pei; Yen, Jui-Lung; Lee, Yann-Jinn; Huang, Chi-Yu; Hung, Han-Yang; Hsu, Chyong-Hsin; Kao, Hsin-An; Chang, Jui-Hsing; Chiu, Nan-Chang; Ho, Che-Sheng; Chao, Mei-Chyn; Niu, Dau-Ming; Tsai, Li-Ping; Kuo, Pao-Lin
國立成功大學 2007-06 Genotype and phenotype in patients with Prader-Willi Syndrome in Taiwan Lin, Hsiang-Yu; Lin, Shuan-Pei; Chuang, Chih-Kuang; Chen, Ming-Ren; Yen, Jui-Lung; Lee, Yann-Jinn; Huang, Chi-Yu; Tsai, Li-Ping; Niu, Dau-Ming; Chao, Mei-Chyn; Kuo, Pao-Lin

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